Bickerstaff brainstem encephalitis is a rare inflammatory disorder of the central nervous system , first described by Edwin Bickerstaff in 1951. It may also affect the peripheral nervous system , and has features in common with both Miller Fisher syndrome and Guillain–Barré syndrome .
12-593: [REDACTED] Look up BBE in Wiktionary, the free dictionary. BBE may refer to: Arts and media [ edit ] B.B.E. , a French trance music group Bad Boy Entertainment , an American hip hop and R&B record label Barely Breaking Even , a British record label Bible in Basic English , a 1949 translation of the Bible Places in
24-721: A British record label Bible in Basic English , a 1949 translation of the Bible Places in the United States [ edit ] Baldwin Beach Express , a highway in Alabama Belgrade-Brooten-Elrosa School District , Minnesota Other uses [ edit ] Bangba language , spoken in DR Congo (ISO 639-3: bbe ) Barako Bull Energy , a Philippine basketball team Bickerstaff brainstem encephalitis ,
36-498: A good recovery. The condition is too rare for controlled trials to have been undertaken. The first cases of bickerstaff brainstem encephalitis were reported in 1951 by Cloake and Bickerstaff under the name “Mesencephalitis and rhombencephalitis”. Edwin Bickerstaff named the disease “brainstem encephalitis” in 1957. The disorder has been known as Bickerstaff’s brainstem encephalitis ever since 1978 when Edwin Bickerstaff wrote
48-505: A rare disease Bijzondere Bijstands Eenheid , a Dutch special forces unit Topics referred to by the same term [REDACTED] This disambiguation page lists articles associated with the title BBE . If an internal link led you here, you may wish to change the link to point directly to the intended article. Retrieved from " https://en.wikipedia.org/w/index.php?title=BBE&oldid=1242096250 " Category : Disambiguation pages Hidden categories: Short description
60-596: Is diagnostic of Bickerstaff brainstem encephalitis. It is, therefore, possible that a proportion of cases are due to other causes, such as infection or lymphoma , but remain undiagnosed. It is also possible that there is more than one autoimmune disease that can cause an illness that would currently be diagnosed as Bickerstaff's. There is certainly overlap between Guillain–Barré syndrome , Miller Fisher syndrome and Bickerstaff brainstem encephalitis, as well as other conditions associated with anti-ganglioside antibodies such as chronic ophthalmoplegia with anti-GQ1b antibody and
72-426: Is different from Wikidata All article disambiguation pages All disambiguation pages BBE [REDACTED] Look up BBE in Wiktionary, the free dictionary. BBE may refer to: Arts and media [ edit ] B.B.E. , a French trance music group Bad Boy Entertainment , an American hip hop and R&B record label Barely Breaking Even ,
84-723: Is different from Wikidata All article disambiguation pages All disambiguation pages Bickerstaff brainstem encephalitis The most frequent initial symptoms of Bickerstaff brainstem encephalitis are drowsiness , gait disturbances , and diplopia . Throughout the course of the disorder, almost every patient develops ataxia and external ophthalmoplegia . Most patients have disturbances of consciousness such as stupor , drowsiness , or coma . Babinski’s sign , facial weakness , pupil abnormalities, bulbar palsy , and nystagmus are also commonly found. Symptoms tend to develop fairly quickly, within one to two days. There have been reports of dysesthesias and limb weakness as
96-435: The United States [ edit ] Baldwin Beach Express , a highway in Alabama Belgrade-Brooten-Elrosa School District , Minnesota Other uses [ edit ] Bangba language , spoken in DR Congo (ISO 639-3: bbe ) Barako Bull Energy , a Philippine basketball team Bickerstaff brainstem encephalitis , a rare disease Bijzondere Bijstands Eenheid , a Dutch special forces unit Topics referred to by
108-450: The pharyngo-cervico-brachial variant of GBS. Anti-GQ1b antibodies have been found in two-thirds of patients with this condition. This antibody is also found in almost all cases of Miller Fisher syndrome. The EEG is often abnormal, but shows only slow wave activity, which also occurs in many other conditions, and so is of limited value in diagnosis. Similarly, raised CSF protein levels and pleocytosis are frequent but non-specific. It
120-415: The presenting features of Bickerstaff brainstem encephalitis. The clinical features and course of the condition, the associated auto-antibodies against relevant antigens , and the response to treatment, all suggest that Bickerstaff brainstem encephalitis is an autoimmune disease . However, each of these criteria fails to fit a substantial proportion of patients, and there is no single test or feature which
132-403: The same term [REDACTED] This disambiguation page lists articles associated with the title BBE . If an internal link led you here, you may wish to change the link to point directly to the intended article. Retrieved from " https://en.wikipedia.org/w/index.php?title=BBE&oldid=1242096250 " Category : Disambiguation pages Hidden categories: Short description
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#1732787784592144-600: Was originally thought that raised CSF protein without pleocytosis ('albuminocytological dissociation') was a characteristic feature, as it is in Guillain–Barré syndrome , but this has not been supported in more recent work. In only 30% of cases is an MRI brain scan abnormal. Nerve conduction studies may show an axonal polyneuropathy . Most patients reported in the literature have been given treatments suitable for autoimmune neurological diseases, such as, plasmapheresis and/or intravenous immunoglobulin , and most have made
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